Tularemia (Francisella tularensis)

 

 

Purpose

 

To recommend procedures for handling potential biological threats of Tularemia exposure.

 

Description of Agent/Syndrome

 

                  1.             Francisella tularensis, the organism that causes tularemia, is one of the most infectious pathogenic bacteria known, requiring inoculation or inhalation of as few as ten (10) organisms to cause disease.

 

                  2.             Francisella tularensis is considered to be a dangerous potential biological weapon because of its extreme infectivity, ease of dissemination and substantial capacity to cause illness and death.

 

3.                           Francisella tularensis is a hardy non-spore forming organism that is capable of surviving for weeks at:

 

                  a)             low temperatures in water

                  b)             moist soil

                  c)              hay

                  d)             straw or

                  e)             decaying animal carcasses

 

4.                           F. tularensis has been divided into two subspecies:

 

                  a)             F. tularensis biovar tularensis (Type A), which is the most common biovar isolated in North America and may be highly virulent in humans and animals.

                  b)             F. tularensis biovar palaearctica (Type B) which is relatively avirulent and thought to be the cause of all human tularemia in Europe and Asia.

 

                  5.             Human-to-human transmission has NOT been documented.

 

                  6.             The United States studied use of this organism as a weapon in the 1950s and 1960s.

 

7.             During World War II, the potential of F. tularensis as a biological weapon was studied by the Japanese and by the U.S. and allies.

 

8.         Tularemia was one of several biological weapons that were stockpiled by the US Military in the late 1960s. All which were destroyed by 1973. The Soviet Union continued weapons production of antibiotic and vaccine resistant strains into the early 1990s.

 

Transmission

 

              1.               Naturally acquired

 

Natural reservoirs include small mammals such as voles, mice, water rats, squirrels, rabbits and hares. Naturally acquired human infection occurs through a variety of mechanisms such as:

 

a)    bites of infected arthropods

b)    handling infectious animal tissues or fluids

c)    direct contact or ingestion of contaminated water, food, or soil

d)    inhalation of infective aerosols

 

NOTE: F. tularensis is so infective that examining an open culture plate can cause infection.

 

2.                              Inhalation Dissemination

              3.               Intentional (possible terrorist action)

 

Incubation

 

1.            Illness beginning three (3) to five (5) days after exposure

2.            Incubation Range: One (1) to fourteen (14) days

 

Signs and Symptoms

 

1.            In the natural setting, tularemia is noted to be a predominately rural disease.

2.            Clinical presentations include: fever, chills, headache, malaise and presents in various

forms:

 

a)    ulceroglandular

b)    glandular

c)    oculogandular

d)    oropharyngeal

e)    pneumonic-pleuropneumonitis develops in a significant portion of cases over days and weeks

f)     typhoidal

g)    septic forms-without antibiotic treatment the clinical course could progress to respiratory failure, shock, death

                 

Diagnosis

 

Rapid diagnosis relies mainly on clinical suspicion. Culture is the only definitive diagnostic test.

 

  1.              Inform Lab personnel of suspected Tularemia.

2.              Physicians who suspect inhalational tularemia should promptly collect specimens of respiratory secretions and blood and alert the laboratory of the need for special diagnostic and safety procedures.

3.              Francisella tularensis grows best in cysteine-enriched broth and thioglycollate broth and on cysteine heart blood agar, buffered charcoal-yeast agar, and chocolate agar.

                  4.              If suspected, Lab should hold culture for 10 days.

 

Treatment & Prophylaxis

 

 

Recommendations for treatment of Patient With Tularemia in a Contained Casualty Setting*

Contained Casualty Recommended Therapy

Adults – preferred choices

Streptomycin, 1 g lM twice daily

Gentamicin, 5 mg/kg IM or IV once daily †

Alternative choices

Doxycycline, 100mg IV twice daily

Chloramphericol, 15 mg/kg IV 4 times daily †

Ciprofloxacin, 400 mg IV twice daily †

 

Children – preferred choices

Streptomycin, 15 mg/kg IM twice daily (should not exceed 2g/d)

Gentamicin, 2.5 mg/kg IM or IV 3 times daily †

 

 

Alternative choices
Doxycycline; if weight ~ 45 kg, 100 mg IV twice daily; if weight <45 kg, give 2.2 mg/kg IV twice daily

Chloramphericol, 15 mg/kg IV 4 times daily †

Ciprofloxacin, 15 mg/kg IV twice daily †

 

Pregnant Women – preferred choices

Gentamicin, 5 mg/kg IM or IV once daily †

Streptomycin, lg lM twice daily

 

Alternative choices
Doxycycline, 100 mg IV twice daily

Ciprofloxacin, 400 mg IV twice daily †

Recommendations for treatment of Patient With Tularemia in a Mass Casualty Setting and for post exposure**

Mass Casualty Recommended Therapy

Adults – preferred choices

Doxycycline, 100 mg orally twice daily

Ciprofloxacin, 500 mg orally twice daily †

 

Alternative choices



Children – preferred choices

Doxycycline if> 45 kg, give 100 mg orally twice daily; if <45 kg, give 2.2 mg/kg orally twice daily

Ciprofloxacin, 15 mg/kg IV orally twice daily †

 

Alternative choices

 

Pregnant Women – preferred choices

Ciprofloxacin, 500 mg orally twice daily †

Doxycycline, 100 mg orally twice daily

 

Alternative choices

 

* Treatment with streptomycin, gentamicin, or ciprofloxacin should be continued for 10 days, treatment with doxycycline or chloramphericol should be continued for 14-21 days. Persons beginning treatment with intramuscular (IM) or intravenous (IV) doxycycline, ciprofloxacin, or chloramphericol can switch to oral antibiotic administration when clinically indicated.

  Not a US Food and Drug Administration-approved use.

 

Ciprofloxacin dosage should not exceed 1 g/d in children.

 

** One antibiotic, appropriate for patient age, should be chosen from among alternatives.  The duration of all recommended therapies in second half of table is 14 days.

 

 

Vaccination is NOT recommended as post-exposure prophylaxis.

 

In the U.S. a live-attenuated vaccine derived from the avirulent Live Vaccine Strain (LVS) has been used to protect laboratory personnel routinely working with F. tularensis.

 

Control Measures and Decontamination

 

1.              Person to person transmission has not been documented

2.              Standard Precautions for patient care and patient care equipment

3.              Routine hospital disinfectants can be used for environmental cleaning.

4.              For laboratory spills, spray the surface with 10% bleach solution (1 part household bleach and 9 parts water). After 10 minutes, clean with 70% alcohol.

5.              Persons with direct exposure to powder or liquid aerosols should shower and launder clothing.

 

Notification

 

Internal: At hospital notify______________________________

 

External:      All suspected cases of suspected Tularemia exposure are Class A3 Reportable and should be reported immediately to the Local Health Department who will then contact the State Health Department and/or CDC.

 

Lab:

 

Due to potential risks associated with handling infectious materials, laboratory testing should be the minimum necessary for diagnostic evaluation and patient care. Laboratory specimens should be placed in plastic bags that are sealed, and then transported in clearly labeled, durable, leak-proof containers directly to the specimen handling area of the laboratory. Care should be taken not to contaminate the external surfaces of the container. Lab personnel should be notified of what they are handling.

 

SPECIMENS

 

TULAREMIA (Francisella tularensis)

Blood Cultures: two separate sets from different sites (one set is 2 bottles – 10 ml each bottle)

2 red-top or gold-top tubes

(for serology)

Sputum

CSF

(if meningeal signs present)

Lymph Node Biopsy or Aspirate (send in anaerobic transport vial)

ID Consult

Note on requisition

Possible F. tularensis exposure in an asymptomatic patient

No

No

No

No

No

No

Not applicable

Tularemia

Yes

Yes

Yes

Yes

Yes

Yes

R/O Tularemia

 

 

 

References

 

Center For Civilian Biodefense Studies: http://www.hopkinsbiodefense.org/pages/center/approach.html

Biodefense Quarterly, December 2000/January 2001-Volume 2, Number 3.

JAMA, June 6 2001-Vol 285, No.21

 

Tularemia Bibliography

 

1.              American Public Health Association. 2000. Tularemia. IN: Chin J, ed. Control of Communicable Diseases Manual. Washington, DC: American Public Health Association; 532-535.

2.              Boyce, JM. 1975. Recent trends in the epidemiology of tularemia in the United States. Journal of Infectious Diseases. 131: 197-199.

3.              Burke, DS. 1977. Immunization against tularemia: Analysis of the effectiveness of live Francisella tularensis vaccine in prevention of laboratory acquired tularemia. Journal of Infectious Diseases. 135:55-60.

4.             Christenson, B. 1984. An outbreak of tularemia in the northern part of central Swenden. Scandinavian Journal of Infectious Diseases. 16-285-290.

5.              Dennis, DT. 1998. Tularemia. In: Wallace, RB.ed. Maxcy-Rosenau-Last Public Health and Preventive Medicine. 14th Edition. Stamford: Appleton & Lange; 354-

357.

6.              Evans, ME, Gregory, DW, Schaffner, W, McGee, ZA. 1985. Tularemia: A 30-year experience with 88 cases. Medicine. 64:251-269.

7.             Francis, E. 1937. Sources of infection and seasonal incidence of tularemia in man. Public Health Reports.52:103-1 13.

8.              Higgins, JA, Hubalek, Z, Halouzka, J, et al. 2000. Detection of Francisella tularensis in infected mammals and vectors using a proble-based polymerase chain reaction. The American Journal of Tropical Medicine and Hygiene. 62:310-318.

9.              Lillite, RD, Francis, El .1937. The pathology of tularaemia in man (Homosapiens). In: The Pathology of Tularaemia. National Institute of Health Bulletin No. 167. Washington, DC: United States Government Printing Office: 1-81.

10.           Mignani, E, Palmieri, F, Fontana, M, Mango, S. 1988. Italian epidemic of waterborne tularaemia. Lancet.ii:1423.

11.           Overholdt, EL, Tigertt, WD, KadulI, PJ, et al. 1961. An analysis of forty-two cases of laboratory-acquired tularemia. American Journal of Medicine. 30:785-806.

12.          Pollitzer, R. 1967. History and incidence of tularemia in the Soviet Union-A review. Institute for Contemporary Russian Studies. Bronx, New York: Fordham University; 1-103.

13.           Pullen, RL, Stuart, BM. 1945. Tularemia: Analysis of 225 cases. Journal of the American Medical Association. 129:495-500.

14.           Russell, P, Eley, SM, Fulop, MJ, Bell, DL, Titball, RW. 1998. The efficacy of ciprofloxacin and doxycycline against tularemia. Journal of Antimicrobial Chemotherapy. 41:461-465.

15.           Saslaw, 5, Eigelsbach, HT, Prior, J, Wilson, HE, Carhart, S. 1961. Tularemia vaccine study.lI. Respiratory challege. Archives of Internal Medicine. 107:134-146.

16.           Saslaw, S, Eigelsbach, HT, Wilson, HE, Prior, JA, Carhart, S.1961. Tularemia vaccine study.l.Intracutaneous challenge. Archives of Internal medicine.

107:121-133.

17.           Sawyer, WD, Dangerfield, HG, Hogge, AL, Crozier, D. 1966. Antibiotic prophylaxis and therapy of airborne tularemia. Bacteriological Reviews.

30:542-548.

18.           Syrjala, H, Sutinen, S. Jokinen, K, Nieminen, P, Tuuponen, T, Salminen, A. 1986. Bronchial changes in airborne tularemia. The Journal of Laryngology Otology. 100:1169-1176.

 

 

Note:     These are guidelines that have been developed with data available as of 5/9/02.

 

 

Initially Prepared by

The Akron Regional Hospital Association

Emergency Preparedness Subcommittee

August 20, 2002